A rare case of osmotic pontine demyelination due to hypokalemia in a patient with Sjogren syndrome and renal tubular acidosis.

9 years old child presented to pediatrics emergency with cyanotic spell and headache. He was a known case of tetralogy of Fallot with a large VSD. On examination – the child had peripheral and central cyanosis.

39 years , male, presented with progressive gait disturbance and speech difficulty since 11 months. Associated with headache, giddiness and vomiting since 3-4 months.